encyclopedia of medical concepts
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Hydrocephalus
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Definition
: Excessive accumulation of cerebrospinal fluid within the cranium which may be associated with dilation of cerebral ventricles, INTRACRANIAL HYPERTENSION; HEADACHE; lethargy; URINARY INCONTINENCE; and ATAXIA.
See Also
Cerebral Ventriculitis
;
Intracranial Hypertension
;
Macrocephaly
Examples
Dandy-Walker Syndrome
;
Hydrocephalus, Normal Pressure
Other names
Post-
Traumatic Hydrocephalus; Obstructive Hydrocephalus; Congenital Hydrocephalus; Communicating Hydrocephalus; Ventriculomegaly, Fetal Cerebral; Ventriculomegaly, Cerebral; Ventriculomegalies, Fetal Cerebral; Ventriculomegalies, Cerebral; Stenosis, Aqueductal; Post Traumatic Hydrocephalus; Hydrocephalus, Post-
Traumatic; Hydrocephalus, Obstructive; Stenoses, Aqueductal; Hydrocephalus, Congenital; Hydrocephalus, Communicating; Hydrocephalus Ex-
Vacuos; Hydrocephalus Ex Vacuo; Fetal Cerebral Ventriculomegalies; Cerebral Ventriculomegaly, Fetal; Cerebral Ventriculomegalies, Fetal
Substance
CAS Registry & name
Categories
Source
Palmer Pagon syndrome
0
*Hydrocephalus
Umbilicus/abnormalities.
Baker Vinters syndrome
0
*Hydrocephalus
*Craniofacial Abnormalities
Cerebral Aqueduct/abnormalities.
Beemer Ertbruggen syndrome
0
*Facies
*Heart Defects, Congenital
*Hydrocephalus
Bone and Bones/abnormalities
Genitalia, Male/abnormalities.
Kozlowski Brown Hardwick syndrome
0
*Abnormalities, Multiple
*Hydrocephalus
Bone and Bones/abnormalities.
Yim Ebbin syndrome
0
*Abnormalities, Multiple
*Cleft Lip
*Coloboma
*Cleft Palate
*Ectromelia
*Hydrocephalus.
Bor-
Duane hydrocephalus contiguous gene syndrome
0
*Duane Retraction Syndrome
*Hydrocephalus
*Branchio-Oto-Renal Syndrome
Carpal Bones/abnormalities.
VACTERL hydrocephaly
0
*Heart Defects, Congenital
*Hydrocephalus
*Limb Deformities, Congenital
Anal Canal/abnormalities
Esophagus/abnormalities
Kidney/abnormalities
Spine/abnormalities
Trachea/abnormalities.
VACTERL association with hydrocephaly, X-
linked
0
*Hydrocephalus
*Heart Defects, Congenital
*Limb Deformities, Congenital
*Genetic Diseases, X-Linked
Anal Canal/abnormalities
Esophagus/abnormalities
Kidney/abnormalities
Spine/abnormalities
Trachea/abnormalities.
Waaler Aarskog syndrome
0
*Hydrocephalus
*Scoliosis
Scapula/abnormalities
Spine/abnormalities.
Clark-
Baraitser syndrome
0
*Growth Disorders
*Hydrocephalus
*Obesity
*Facies
*Mental Retardation, X-Linked.
Hydrolethalus syndrome
0
*Hand Deformities, Congenital
*Heart Defects, Congenital
*Hydrocephalus.
Hydrocephalus, X-
linked
0
*Hydrocephalus
*Genetic Diseases, X-Linked
Cerebral Aqueduct/abnormalities.
Cole Carpenter syndrome
0
*Craniosynostoses
*Eye Abnormalities
*Hydrocephalus
*Osteogenesis Imperfecta.
Hydrocephalus, endocardial fibroelastosis, and cataracts
0
*Cataract
*Endocardial Fibroelastosis
*Hydrocephalus.
Schwartz Cohen-
Addad Lambert syndrome
0
*Hydrocephalus
*Melanosis/congenital
*Meningomyelocele.
Daish Hardman Lamont syndrome
0
*Growth Disorders
*Hydrocephalus
*Joint Instability
*Kyphosis
*Scoliosis.
Daentl Towsend Siegel syndrome
0
*Hydrocephalus
*Nephritis, Hereditary
*Scleral Diseases.
Iris dysplasia hypertelorism deafness
0
*Abnormalities, Multiple
*Hydrocephalus
*Facies
*Hearing Loss
Anterior Chamber/abnormalities.
Game Friedman Paradice syndrome
0
*Foot Deformities, Congenital
*Growth Disorders
*Hydrocephalus
*Craniofacial Abnormalities
Intestines/abnormalities.
Aase Smith syndrome
0
*Abnormalities, Multiple
*Cleft Palate
*Contracture
*Hydrocephalus
*Limb Deformities, Congenital.
Radius absent anogenital anomalies
0
*Bone Diseases, Developmental
*Hydrocephalus
*Hypospadias
*Genetic Diseases, X-Linked
Fingers/abnormalities
Radius/abnormalities.