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Tooth Abnormalities
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Definition
: Congenital absence of or defects in structures of the teeth.
do not use /congen & do not coord with INFANT, NEWBORN, DISEASES; duplication of teeth
Examples
Anodontia
;
Dens in Dente
;
Dental Enamel Hypoplasia
;
Dentin Dysplasia
;
Dentinogenesis Imperfecta
;
Fused Teeth
;
Odontodysplasia
;
Tooth, Supernumerary
Other names
Tooth Abnormality; Teeth Abnormality; Odontomes; Abnormality, Tooth; Abnormality, Teeth; Teeth Abnormalities; Abnormalities, Tooth; Abnormalities, Teeth; Odontome
Substance
CAS Registry & name
Categories
Source
Deafness with Labyrinthine Aplasia Microtia and Microdontia (LAMM)
0
*Deafness/congenital
*Tooth Abnormalities
Ear/abnormalities.
Nance-
Horan syndrome
0
*Cataract/congenital
*Tooth Abnormalities
*Genetic Diseases, X-Linked.
Ackerman syndrome
0
*Glaucoma
*Tooth Abnormalities
*Maxillofacial Abnormalities.
Lacrimoauriculodentodigital syndrome
0
*Syndactyly
*Abnormalities, Multiple
*Lacrimal Apparatus Diseases
*Tooth Abnormalities
*Hearing Loss.
Larsen syndrome, dominant type
0
*Cleft Lip
*Cleft Palate
*Dislocations/congenital
*Osteochondrodysplasias
*Tooth Abnormalities
*Craniofacial Abnormalities.
Odontomicronychial dysplasia
0
*Ectodermal Dysplasia
*Nail Diseases
*Tooth Abnormalities.
Grubben de Cock Borghgraef syndrome
0
*Developmental Disabilities
*Eczema/congenital
*Muscle Hypotonia/congenital
*Tooth Abnormalities
*Limb Deformities, Congenital.
AREDYLD Syndrome
0
*Ectodermal Dysplasia
*Diabetes Mellitus, Lipoatrophic
*Tooth Abnormalities.
KBG syndrome
0
*Abnormalities, Multiple
*Bone Diseases, Developmental
*Intellectual Disability
*Tooth Abnormalities
*Facies.
Temtamy preaxial brachydactyly syndrome
0
*Deafness
*Intellectual Disability
*Mouth Abnormalities
*Tooth Abnormalities
*Brachydactyly.
Teeth noneruption of with maxillary hypoplasia and genu valgum
0
*Abnormalities, Multiple
*Tooth Abnormalities
*Genu Valgum
Maxilla/abnormalities
Zygoma/abnormalities.
Taurodontism, microdontia, and dens invaginatus
0
*Mouth Abnormalities
*Tooth Abnormalities.
Oral Surg Oral Med Oral Pathol. 1978 Jan;45(1):107-12
Taurodontism
0
*Tooth Abnormalities
Dental Pulp Cavity/abnormalities.
Zazam Sheriff Phillips syndrome
0
*Ectopia Lentis
*Intellectual Disability
*Tooth Abnormalities
*Aniridia.
Weyers acrofacial dysostosis
0
*Abnormalities, Multiple
*Tooth Abnormalities
*Limb Deformities, Congenital.
Tricho-
dento-
osseous syndrome 1
0
*Abnormalities, Multiple
*Bone Diseases
*Craniofacial Dysostosis
*Hair Diseases
*Tooth Abnormalities.
CODAS syndrome
0
*Eye Abnormalities
*Growth Disorders
*Hip Dislocation, Congenital
*Osteochondrodysplasias
*Tooth Abnormalities
*Craniofacial Abnormalities.
Blepharo-
cheilo-
dontic syndrome
0
*Cleft Lip
*Cleft Palate
*Ectropion
*Tooth Abnormalities.
Fused mandibular incisors
0
*Tooth Abnormalities.
Rodrigues blindness
0
*Blindness/congenital
*Growth Disorders
*Hair Diseases
*Tooth Abnormalities.
J Med Genet. 1992;29(5):323-5
Euhidrotic ectodermal dysplasia
0
*Ectodermal Dysplasia
*Hyperopia
*Tooth Abnormalities.
Iridogoniodysgenesis, dominant type
0
*Eye Abnormalities
*Glaucoma
*Iris Diseases
*Tooth Abnormalities
Anterior Chamber/abnormalities.