Definition: The beta subunit of hexosaminidase A and hexosamininidase B. Mutations in the gene that encodes this protein are linked to SANDHOFF DISEASE and can result in loss of both hexosaminidase A activity and hexosaminidase B activity.
Other names beta N Acetylhexosaminidase beta Chain; beta Hexosaminidase beta Chain; beta Chain, beta-N-Acetylhexosaminidase; beta Chain, beta-Hexosaminidase; beta-N-Acetylhexosaminidase beta Chain; Hexosaminidase B, beta Chain; Hexosaminidase A, beta Chain