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Lymphohistiocytosis, Hemophagocytic
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Definition
: A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.
Other names
Hemophagocytic Lymphohistiocytosis; Hemophagocytic Lymphohistiocytoses, Primary; Hemophagocytic Lymphohistiocytoses, Familial; Hemophagocytic Lymphohistiocytoses; Hemophagocytic Lymphocytosis, Familial; Hemophagocytic Lymphocytoses, Familial; Familial Histiocytic Reticuloses; Familial Hemophagocytic Lymphohistiocytosis; Familial Hemophagocytic Lymphohistiocytoses; Familial Hemophagocytic Lymphocytoses; Familial Erythrophagocytic Lymphohistiocytoses; Erythrophagocytic Lymphohistiocytosis, Familial; Erythrophagocytic Lymphohistiocytoses, Familial; Primary Hemophagocytic Lymphohistiocytosis; Hemophagocytic Lymphohistiocytosis Familial -
1; Familial Histiocytic Reticulosis; Familial Erythrophagocytic Lymphohistiocytosis; Reticulosis, Familial Histiocytic; Reticuloses, Familial Histiocytic; Primary Hemophagocytic Lymphohistiocytoses
Substance
CAS Registry & name
Categories
Source
Hemophagocytic lymphohistiocytosis, familial, 4
0
*Lymphohistiocytosis, Hemophagocytic.
Hemophagocytic lymphohistiocytosis, familial, 3
0
*Lymphohistiocytosis, Hemophagocytic.
Hemophagocytic lymphohistiocytosis, familial, 2
0
*Lymphohistiocytosis, Hemophagocytic.