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gamma-Butyrobetaine Dioxygenase
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Definition
: An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.
Other names
gamma Butyrobetaine,2 Oxoglutarate Dioxygenase; gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase; gamma Butyrobetaine Hydroxylase; gamma Butyrobetaine Dioxygenase; Hydroxylase, gamma-
Butyrobetaine; Hydroxylase, Trimethylaminobutyrate; Hydroxylase, Butyrobetaine; Dioxygenase, gamma-
Butyrobetaine,2-
Oxoglutarate; Dioxygenase, gamma-
Butyrobetaine; Dioxygenase gamma-
Butyrobetaine, 2-
Oxoglutarate; 2-
Oxoglutarate Dioxygenase gamma-
Butyrobetaine; gamma-
Butyrobetaine,2-
Oxoglutarate Dioxygenase; gamma-
Butyrobetaine, 2-
Oxoglutarate Dioxygenase; gamma-
Butyrobetaine Hydroxylase; Trimethylaminobutyrate Hydroxylase; Butyrobetaine Hydroxylase; 4-
Trimethylaminobutyrate, 2-
Oxoglutarate Oxygen Ox
Substance
CAS Registry & name
Categories
Source
Drugs
*
4-
trimethylaminobutyric acid dioxygenase, mouse
EC 1.14.11.1
*gamma-Butyrobetaine Dioxygenase.
Anal Biochem. 2006 Jul 1;354(1):132-9