Definition: Progressive myopathies characterized by the presence of inclusion bodies on muscle biopsy. Sporadic and hereditary forms have been described. The sporadic form is an acquired, adult-onset inflammatory vacuolar myopathy affecting proximal and distal muscles. Familial forms usually begin in childhood and lack inflammatory changes. Both forms feature intracytoplasmic and intranuclear inclusions in muscle tissue. (Adams et al., Principles of Neurology, 6th ed, pp1409-10)
do not coord with INCLUSION BODIES but coord with INCLUSION BODIES, VIRAL if relevant (IM or NIM)
Other names Myositides, Inclusion Body; Inclusion Body Myositides; Sporadic Inclusion Body Myositis; Myositis, Inclusion Body, Sporadic; Inclusion Body Myositis, Sporadic; Inclusion Body Myopathy, Sporadic; Myopathy, Inclusion Body, Sporadic; Inclusion Body Myositis
