Definition: A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.
Other names Pseudohypoaldosteronism, Type II; Pseudohypoaldosteronism, Type I, Autosomal Recessi; Pseudohypoaldosteronism, Type I, Autosomal Dominan; Pseudohypoaldosteronism, Type I; Pseudohypoaldosteronism Type 1, Autosomal Recessiv; Pseudohypoaldosteronism Type 1; Hypertensive Hyperkalemia, Familial; Hyperpotassemia and Hypertension, Familial; Gordon Hyperkalemia-Hypertension Syndrome; Type II Pseudohypoaldosteronisms; Type II Pseudohypoaldosteronism; Type I Pseudohypoaldosteronisms; Type I Pseudohypoaldosteronism; Type 2s, Pseudohypoaldosteronism; Type 2, Pseudohypoaldosteronism; Type 1s, Pseudohypoaldosteronism; Type 1, Pseudohypoaldosteronism; Syndrome, Gordon Hyperkalemia-Hypertension; Pseudohypoaldosteronisms, Type II; Pseudohypoaldosteronisms, Type I
