encyclopedia of medical concepts
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Iduronate Sulfatase
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Definition
: An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.
See Also
Mucopolysaccharidosis II
Other names
Sulfoiduronate Sulfatase; Iduronatesulfate Sulfohydrolase; Hunter Corrective Factor; Sulfohydrolase, Iduronatesulfate; Sulfate Sulfatase, Iduronate; Sulfatase, Sulfoiduronate; Sulfatase, Iduronate Sulfate; Sulfatase, Iduronate; Factor, Hunter Corrective; Corrective Factor, Hunter; Iduronate Sulfate Sulfatase
Drugs
*
:
ELAPRASE
Substance
CAS Registry & name
Categories
Source
Drugs
*
idursulfase
EC 3.1.6.13
*Iduronate Sulfatase.
FDA Consum 2006 Nov-Dec;40(6):5