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G(M1) Ganglioside

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Definition: A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis.      Other names Monosialosyl Tetraglycosyl Ceramide; Tetraglycosyl Ceramide, Monosialosyl; Monosialoganglioside, GM1a; Ceramide, Monosialosyl Tetraglycosyl; GM1a Monosialoganglioside
 
SubstanceCAS Registry & nameCategoriesSourceDrugs*
fucosyl(galactosyl)-ganglioside GM1  0   G(M1) Ganglioside/*analogs & derivatives. Biochem J 2007 Oct 1;407(1):31-40
ganglioside GM1alpha  0   G(M1) Ganglioside/*analogs & derivatives. Carbohydr Res 2005 Feb 7;340(2):211-20
3'-O-sulfo-ganglioside M1b  0   *Sulfates G(M1) Ganglioside/*analogs & derivatives. Carbohydr Res 2002 Oct 8;337(18):1679-86
9-((((2-(125I)iodo-4-((trifluoromethyl)-3H-diazirin-3-yl)benzyl)oxy)carbonyl)nonanoyl)-GM1 ganglioside  0   G(M1) Ganglioside/*analogs & derivatives Iodine Radioisotopes. Glycoconj J 2000 Mar-Apr;17(3-4):215-22
fucosyl-N-acetylgalactosaminyl-GM1  0   G(M1) Ganglioside/*analogs & derivatives. J Biochem (Tokyo) 1999 Nov;126(5):962-8
lyso-fucosyl GM1  0   G(M1) Ganglioside/*analogs & derivatives. J Biochem (Toyko) 1997 Feb;121(2):264-9
LIGA 20  126586-85-4 Acetamide, N-(1-(((O-(N-acetyl-alpha-neuraminosyl)-(2-3)-O-(O-beta-D-galactopyranosyl-(1-3)-2-(acetylamino)-2-deoxy-beta-D-galactopyranosyl-(1-4))-O-beta-D-galactopyranosyl-(1-4)-beta-D-glucopyranosyl)oxy)methyl)-2-hydroxy-3-heptadecenyl)-2,2-dichloro-,   G(M1) Ganglioside/*analogs & derivatives Sphingosine/*analogs & derivatives. Neurology 1994 Apr;44(4):748-50
LIGA 4  0   G(M1) Ganglioside/*analogs & derivatives Sphingosine/*analogs & derivatives. Neurology 1994 Apr;44(4):748-50
ganglioside AGF44  131129-98-1   G(M1) Ganglioside/*analogs & derivatives. Drugs Exp Clin Res 1992;18(6):251-9
5-(4-(3-(trifluromethyl)diazirinyl)phenyl)pentanoyl-lyso-G(M1) ganglioside  131966-72-8   G(M1) Ganglioside/*analogs & derivatives. Chem Phys Lipids 1990;55(2):103
lactosaminyl-G(M1)  129898-66-4   G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1990;265(24):1433
ganglioside GD1alpha  101839-44-5   G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1990;265(14):8144
N-parinaroylganglioside G(M1)  120418-73-7   G(M1) Ganglioside/*analogs & derivatives. Biochemistry 1989;28(10):4195
ganglioside M1 lactone  103220-36-6   G(M1) Ganglioside/*analogs & derivatives. J Neurochem 1989;53(3):747
12-((4-azido-2-nitrophenyl)amino)dodecanoyl-GM1  116926-94-4   G(M1) Ganglioside/*analogs & derivatives. Biochemistry 1989;28(1):77
galactose(fucose)asialo-GM1 glycolipid  0   *G(M1) Ganglioside. J Biol Chem 1989;264(6):3409
IV(4)-galactosyl-N-acetylganglioside M1b  76828-87-0   G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1988;263(9):4369
ganglioside AGF2  100345-64-0   G(M1) Ganglioside/*analogs & derivatives. Stroke 1987;18(1):184
fucosyl GM1 ganglioside  71812-11-8   G(M1) Ganglioside/*analogs & derivatives. J Biochem (Tokyo) 1983;94(1):1
monosialosyltriglycosylceramide (sulfated)  0   G(M1) Ganglioside/*analogs & derivatives. Eur J Biochem 1981;119(3):647
dansyl oligoganglioside G(M1)  0   *Dansyl Compounds G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1981;256(11):5489
oligoganglioside G(M1)  0   G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1981;256(11):5489
ganglioside M1b  57576-20-2 ganglioside GM1b  G(M1) Ganglioside/*analogs & derivatives. Lipids 1981;16(1):72
lysoGM1 ganglioside  0   G(M1) Ganglioside/*analogs & derivatives. Eur J Biochem 1981;113(2):249
DA-G(M1) ganglioside  0   G(M1) Ganglioside/*analogs & derivatives. J Biol Chem 1980;255(16):7657
choleragen receptor  0   *G(M1) Ganglioside *Receptors, Cell Surface Cholera Toxin. J Biol Chem 1980;255(6):2549
asialo GM1 ganglioside  71012-19-6   *G(M1) Ganglioside. Biochim Biophys Acta 572(1):105;1979; J Immunol 1980;124(1):199; N Engl J Med 1980;302(12):674; N Engl J Med 1980;302(12):686

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Sources: NLM Medical Subject Headings, NIH UMLS, Drugs@FDA, FDA AERS original data copyright United States Government. No endorsement implied. Last modified 6/6/2012

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