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Fumarate Hydratase
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Definition
: An enzyme that catalyzes the reversible hydration of fumaric acid to yield L-malic acid. It is one of the citric acid cycle enzymes. EC 4.2.1.2.
Other names
Fumarase; Hydratase, Fumarate
Substance
CAS Registry & name
Categories
Source
Drugs
*
Fumaric aciduria
0
*Metabolism, Inborn Errors
*Muscle Hypotonia
*Psychomotor Disorders
Fumarate Hydratase/deficiency.
diamminechloro(pyridine)platinum(I)
0
*Organoplatinum Compounds
Fumarate Hydratase/antagonists & inhibitors.
Drug Metabol Drug Interact 1995;12(2):105-15
chloro(1,2-
cyclohexanediamine-
N,N')((methylsulfinyl)benzene-
S)platinum(I)
124578-26-3
*Organoplatinum Compounds
Fumarate Hydratase/antagonists & inhibitors.
Drug Metabol Drug Interact 1995;12(2):105-15
fumarase C
EC 4.2.1.-
*Fumarate Hydratase.
Nat Struct Biol 1995 Aug;2(8):654-62
2,3-
dicarboxyaziridine
57528-68-4
*Aziridines
Fumarate Hydratase/antagonists & inhibitors.
J Biol Chem 1985;260(11):6684