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Dysgammaglobulinemia
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Definition
: An immunologic deficiency state characterized by selective deficiencies of one or more, but not all, classes of immunoglobulins.
coord IM with specific immunoglobulin /defic (IM) but note IGA DEFICIENCY and IGG DEFICIENCY are available; AGAMMAGLOBULINEMIA is also available
Examples
Hyper-IgM Immunodeficiency Syndrome
;
IgA Deficiency
;
IgG Deficiency
Other names
Dysgammaglobulinemias
Substance
CAS Registry & name
Categories
Source
Epilepsy telangiectasia
0
*Dysgammaglobulinemia
*Epilepsy
*Intellectual Disability
*Telangiectasis.