Cystathionine beta-Synthase (definition)

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ψ	Cystathionine beta-Synthase

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Definition: A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyzes the reaction of homocysteine with serine to form cystathionine with the elimination of water. Deficiency of this enzyme leads to HYPERHOMOCYSTEINEMIA and HOMOCYSTINURIA. EC 4.2.1.22.

/defic: consider also HOMOCYSTINURIA or HYPERHOMOCYSTEINEMIA
See Also Homocystinuria

Other names beta-Thionase; Serine Sulfhydrase; beta-Synthase, Cystathionine; beta Thionase; Synthetase, Cystathionine; Sulfhydrase, Serine; Cystathionine beta Synthase; Cystathionine Synthetase

Substance	CAS Registry & name	Categories	Source	Drugs*
CDCP2 protein, Arabidopsis	EC 4.2.1.22	Cystathionine beta-Synthase Arabidopsis Proteins.	Acta Crystallogr Sect F Struct Biol Cryst Commun. 2008 Sep 1;64(Pt 9):825-7

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Sources: NLM Medical Subject Headings, NIH UMLS, Drugs@FDA, FDA AERS original data copyright United States Government. No endorsement implied. Last modified 6/6/2012
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