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Argininosuccinate Lyase
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Definition
: An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.
See Also
Argininosuccinic Aciduria
Examples
delta-Crystallins
Other names
Argininosuccinase; Lyase, Argininosuccinate
Substance
CAS Registry & name
Categories
Source
Drugs
*
argH protein, E coli
EC 4.3.2.1.
*Argininosuccinate Lyase
*Escherichia coli Proteins.
Curr Microbiol 2001 Oct;43(4):260-4
Arg4 protein, S cerevisiae
EC 4.3.2.1
*Argininosuccinate Lyase
*Saccharomyces cerevisiae Proteins.
Yeast 1994 Mar;10(3):309-17
arginine synthetase system
0
*Argininosuccinate Lyase
*Argininosuccinate Synthase
*Multienzyme Complexes.
Clin Nephrol 6(3):240;1975; Folia Psychiatr Neurol Jpn 29(1):77;1975; J Biol Chem 234:1769;1959; Kidney Int (Suppl) 7(3):S280;1975; Tohoku J Exp Med 127(4):379;1979