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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis
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Definition
: Group of systemic vasculitis with a strong association with ANCA. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.
Examples
Churg-Strauss Syndrome
;
Microscopic Polyangiitis
;
Wegener Granulomatosis
Other names
Vasculitis, Pauci-
Immune; Vasculitis, ANCA-
Associated; Vasculitides, Pauci-
Immune; Vasculitides, ANCA-
Associated; Vasculitide, ANCA-
Associated; Pauci-
Immune Vasculitides; Pauci Immune Vasculitis; Anti Neutrophil Cytoplasmic Antibody Associated Va; ANCA-
Associated Vasculitide; ANCA Associated Vasculitis; ANCA Associated Vasculitides; Pauci-
Immune Vasculitis; ANCA-
Associated Vasculitis; ANCA-
Associated Vasculitides