Definition: A sarcoma of young, often female, adults of the lower extremities and acral regions, intimately bound to tendons as circumscribed but unencapsulated melanin-bearing tumors of neuroectodermal origin. An ultrastructural finding simulates flattened and curved barrel staves, corresponding to the internal structures of premelanosomes. There is a 45-60% mortality in clear cell sarcoma. (Segen, Dictionary of Modern Medicine, 1992)
/blood supply /chem /second /secret /ultrastruct permitted; coord IM with precoord organ/neopl term (IM)
Other names Melanoma, Malignant, of Soft Parts; Sarcomas, Clear Cell; Clear Cell Sarcomas; Clear Cell Sarcoma
